Duplicate Bladder Exstrophy With Fistula: A Rare Variant of Exstrophy-Epispadias Complex
نویسندگان
چکیده
Variants of exstrophy are rare anomalies seen in the spectrum bladder exstrophy-epispadias complex. A seven day old male neonate was admitted our department with a variant duplicate communicating fistula. Patient presented patch exstrophic just below low set umbilicus normal sized phallus and normally positioned urethral meatus. The baby managed successfully surgery is under regular follow up.
منابع مشابه
Bladder exstrophy-epispadias complex.
The bladder exstrophy-epispadias complex (BEEC) represents an anterior midline defect with variable expression comprising a spectrum of anomalies involving the abdominal wall, pelvis, urinary tract, genitalia, and occasionally the spine and anus. The vast majority of BEEC cases are classified as non-syndromic and the etiology of this malformation is still unknown. This review presents the curre...
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Introduction Exstrophy and epispadias are part of a spectrum of anomalies characterised by exposure of part or all of the mucosa of the lower urinary tract (bladder and urethra) to the external environment through a defect in the anterior abdominal wall. At one end of this spectrum is cloacal exstrophy, which is the most complex of these anomalies. It is characterised by exposure of the bladder...
متن کاملThe Exstrophy-epispadias complex
Exstrophy-epispadias complex (EEC) represents a spectrum of genitourinary malformations ranging in severity from epispadias (E) to classical bladder exstrophy (CEB) and exstrophy of the cloaca (EC). Depending on severity, EEC may involve the urinary system, musculoskeletal system, pelvis, pelvic floor, abdominal wall, genitalia, and sometimes the spine and anus. Prevalence at birth for the whol...
متن کاملTrue Duplicate Bladder Exstrophy
A three months male child was admitted in our department as a rare variant of bladder exstrophy (true duplicate bladder exstrophy). There are only 8 cases of this variant reported in the literature so far, we report an additional case to add the scarce literature.
متن کاملModern Management of the Exstrophy-Epispadias Complex
The exstrophy-epispadias complex is a rare spectrum of malformations affecting the genitourinary system, anterior abdominal wall, and pelvis. Historically, surgical outcomes were poor in patients with classic bladder exstrophy and cloacal exstrophy, the two more severe presentations. However, modern techniques to repair epispadias, classic bladder exstrophy, and cloacal exstrophy have increased...
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ژورنال
عنوان ژورنال: Journal of Nepal Paediatric Society
سال: 2021
ISSN: ['1990-7982', '1990-7974']
DOI: https://doi.org/10.3126/jnps.v41i2.30752